连枷臂综合征1例报告并文献复习

doi:10.13481/j.1671-587x.20160630

Abstract

Abstract:

Objective: To analyze the clinical materials of one patient with flail arm syndrome (FAS), and to provide evidence for its clinical diagnosis and treatment.Methods: The neurological examination,MRI of cranial,cervical and lumbar, and electromyogram (EMG) were performed in the patient and the patient was clinically diagnosed as FAS; the FAS patient was given the treatment to improve the circulation and nourish the nerves.At the same time, comparative analysis of the results between this case report and other case reports of FAS was performed.Results: The patient was diagnosed as FAS after neurological examination and accessory examination:after symptomatic treatment,the condition of patient had the continuous progress,and the upper extremities of the patient were heavier than those of the lower extremities.The patient died of phlegm blocking airway 9 months after discharged.Conclusion: The patients with bilateral symmetric proximal upper extremities weakness and atrophy should be considered as FAS after the other factors are excluded by EMG and imaging examinations.

Key words: flail arm syndrome, motor neuron disease, iconography, amyotrophic lateral sclerosis, electromyography

CLC Number:

R741

WANG Sijian, CHEN Jiajun, QI Xinchang, GAO Heming, PANG Suisui, SANG Qiuling. Flail arm syndrome: A case report and literature review[J].Journal of Jilin University Medicine Edition, 2016, 42(06): 1203-1206.

References

[1] Hu MT,Ellis CM,All-Chalabi A,et al. Flail arm syndrome:a distinctive variant of amyotrophic lateral sclerosis[J]. J Neurol Neurosurg Psychiatry,1998,65(6):950-951.
[2] Czaplinski A,Strobel W,Gobbi C,et al.Respiratory failure due to bilateral diaphragm palsy as an early manifestation of ALS[J].Med Sei Monit,2003,9(5):34-36.
[3] Hübers A,Hildebrandt V,Petri S,et al.Clinical features and differential diagnosis of flail arm syndrome[J].J Neurol,2016,263(2):390-395.
[4] Khandelwal DC.Owl's eye sign:A rare neuroimaging finding in flail arm syndrome[J].Neurology,2015,85(22):1996.
[5] Kuwahara H,Uchihara T,Kawamura M.An autopsy case of amyotrophic lateral sclerosis presenting with flail arm syndrome and rapid progression of respiratory failure[J].Brain Nerve,2015,67(5):639-650.
[6] Hino S,Sasaki S.Flail arm syndrome with cytoplasmic vacuoles in remaining anterior horn motor neurons:A peculiar variant of amyotrophic lateral sclerosis[J].Neuropathology,2015,35(6):582-586.
[7] Kumar S,Mehta VK,Shukla R.Owl's eye sign:A rare neuroimaging finding in flail arm syndrome[J].Neurology,2015,84(14):1500.
[8] Yoon BN,Choi SH,Rha JH,et al.Comparison between flail arm syndrome and upper limb onset Amyotrophic lateral sclerosis:clinical features and electromyographic findings[J].Exp Neurobiol,2014,23(3):253-257.
[9] Couratier P,Truong C,Khalil M,et al.Clinical features of flail arm syndrome[J].Muscle And Nerve,2000,23(4):646-648.
[10] 刘小璇,樊东升,张俊.ALS患者19例发病后行颈椎手术的随访观察[J].中华神经科杂志,2008,6(41):385.
[11] 苏曼,童晓欣,连枷臂综合征1例报道[J].中风与神经疾病杂志,2010,27(7):662.
[12] Valentino P,Conforti F JJ,Pinjlano D,et al.Brachial amy-oirophic diplegia associated with novel SOD1mutation (L106P)[J].Neurology,2005,64(8):1477-1478.
[13] 王秀丽,叶静纳,董铭,等.连枷臂综合征1例报告[J].中风与神经疾病杂志,2015,32(10):948.

Flail arm syndrome: A case report and literature review

PDF (PC)

Like

Knowledge

Abstract

Cite this article

share this article

References

Related Articles 4

Metrics

Comments

Recommended 0

[1]	LIN Yu, LIU Meihan, SHI Weidong, SUN Zhixia, CHEN Enqi, ZHANG Xin, WANG Zhiyuan. Application of ultrasonography in diagnosis and differential diagnosis of Takayasu arteritis [J]. Journal of Jilin University Medicine Edition, 2017, 43(06): 1268-1271.
[2]	YUAN Huibin, LI Ruijun, ZHANG Zhixin, CHEN Lei, WANG Shuang, HOU Haixin, LIU Zhigang. Evaluation on clinical therapeutic effect of small incision releasing of transverse carpal ligament in treatment of mild and moderate carpal tunnel syndrome [J]. Journal of Jilin University Medicine Edition, 2015, 41(02): 397-400.
[3]	ZHANG Su,GUO Feng,WANG Nian-hui. Analysis on characteristics of surface electromyography of limb muscle fatigue induced by isokinetic flexion and extension movement [J]. Journal of Jilin University Medicine Edition, 2014, 40(06): 1241-1246.
[4]	PANG Zi-qian, YE Yu-qin， LI Qiu-ming. Application values of electromyography in diagnosis and differential diagnosis of diabetic polyneuropathy and alcoholic peripheral neuropathy [J]. Journal of Jilin University Medicine Edition, 2014, 40(06): 1247-1251.