Abstract: Objective: To analyze the clinical features, imaging characteristics and treatment of the male elderly patient with atypical choroid plexus papilloma(ACPP) in the suprasellar region existing impaired vision as main symptom, and to provide the basis for the diagnosis and treatment of the disease. Methods: The clinical data of a patient with ACPP in the suprasellar region existing impaired vision as main symptom were collected, and the clinical features, diagnosis and treatment of ACPP were analyzed, and the relative literatures were reviewed. Results: A 61-year-old male patient was admitted to the hospital with a more than 1 year history of headache and a more than 2 months history of progressive decline in binocular vision. The laboratory examination results revealed that the serum cortisol contents at 00:00 and 8:00 were decreased. The results of brain magnetic resonance imaging (MRI) examination showed a 3.2 cm×2.7 cm×2.0 cm oval mass in the suprasellar region with inheterogeneous hypointensity on T1WI and inheterogeneous hyperintensity on T2WI.The enhanced scranning results showed that the lesion exhibited mixed hypointensity and hyperintensity with blocky in shape and flower ring-like ehancement in its surrounding. The results of laboratory examination and MRI indicated that diagnosis of glioma was not excluded. The patient underwent semi-elective operation and the tumor was resected completely; the pathological diagnosis was ACPP. The patient did not receive radiotherapy or chemotherapy after operation. There was no recurrence after follow-up. Conclusion: ACPP is a kind of low grade malignant tumor without specific imaging findings. Total resection is an effective treatment. Pathological diagnosis is the gold standard for the diagnosis of ACPP. The patients with ACPP diagnosed by pathology should regularly receive reexamination after operation.

Key words: atypical choroid plexus papilloma, choroid plexus papilloma in suprasellar region, choroid plexus neoplasms, suprasellar region