Abstract: Objective: To explore the clinical manifestations,diagnosis points and differential diagnosis of the patient with nevus of ota complicated with Posner-Schlossman syndrome(PSS), and to improve clinicians' understanding of the disease. Methods: The clinical materials of a patient with nevus of ota complicated with PSS were collected; slit-lamp microscope,ultrasound biomicroscope,perimeter,gonioscope and other instruments were used for inspection, the examination results and diagnosis and treatment process of this patient were summarized, and the relevant literatures were reviewed. Results: The male patient,15 years old, went to hospital because of "blurred vision and redness in the right eye",the patient's right temporal, cheek, nose and forehead skin showed blue and black pigmented plaques;the eye examination results showed that the intraocular pressure of the patient's right eye was increased,and there were conjunctival hyperemia, peripheral pigmentation of the sclera, mild corneal edema in right eye and 3 mutton fat isolated keratic precipitates(KPs) behind the cornea. The gonioscope examination results showed that the angle of anterior chamber was open,and trabecular meshwork and ciliary body had extensive pigmentation. Clinical diagnosis was nevus of ota complicated with PSS; the patient was given symptomatic treatment of lowering intraocular pressure and anti-inflammatory, and the patient recovered well. The patient was followed up for 2 years and recurred once, and was given symptomatic treatment again and the symptoms were improved. Conclusion: Increased intraocular pressure is a common serious complication of nevus of ota. This patient had blurred vision and increased intraocular pressure, which was easy to be misdiagnosed as nevus of ota complicated with glaucoma.A diagnosis of PSS should be made based on the clinical manifestations and eye examinations, so as not to delay treatment.

Key words: nevus of ota, Posner-Schlossman syndrome, glaucoma, intraocular pressure, keratic precipitates